Portuguese Version

Year:  1996  Vol. 62   Ed. 6 - ()

Artigos Originais

Pages: 477 to 482

Otologic Manifestations of Pachyonichya Congenita Syndrome.

Author(s): Maria Helena Guatimosin*,
Rogério de Leão Bensadon*,
Tanit Ganz Sanchez**,
Richard Louis Voegels**,
Ricardo Ferreira Bento***.

Keywords: Dermatosis, otologic lesions

The authors report a case of a patient with Pachyonichya Congenita Syndrome, a rare genodermatosis inherited as an autossomic dominant trait, who also had otologic lesions beyond the other classic signs and symptoms of the syndrome. Many kinds of treatment have already been proposed, but all failed to show satisfactory results. A new, cheap and easy-to-use treatment was developed in this study, using keratoblastics interpolated with humectant lotion for 90 days. The results after3 yean of follow-up are still thoroughly satisfactory.






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