Year: 1998 Vol. 64 Ed. 3 - (8º)
Relato de Casos
Pages: 265 to 269
Polyposis and the Peutz Jeghers. Syndrome.
Author(s):
Arthur Guilherme L. B. S. Augusto*;
Lídio Granato**;
Giulio C. Santo***,
Daniel Destailleur****;
Roberto M. Yoshikae*****.
Keywords: Peutz Jeghers syndrome, nasal polyps, hamartoma
Abstract:
The Peutz-Jeghers Syndrome is an autosomal dominant disorder eharaeterized by gastrointestinal polyps and mucocutaneous pigmentation. Rarely the nasal cavity is involved. The authors report two cases of Peutz Jeghers Syndrome with nasal poliposis and a review of some salient features of this entity is made.
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